BACKGROUND AND PURPOSE: Cerebellar hemangioblastomas (HBs) are traditionally classified into different morphologic types: cystic and. Hemangioblastomas (capilliary hemangioblastomas) are tumors of the central nervous system that originate from the vascular system usually during middle- age. The occurrence of cerebral hemangioblastoma in a patient with on Hippel-Lindau disease is very rare. In , Rochat described a cerebral hemangioblastoma.

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Haemangioblastoma (central nervous system) | Radiology Reference Article |

Receive exclusive offers and updates from Oxford Academic. Report of a rare case and review of literature. Spontaneous regression of two putative supratentorial haemangioblastomas in one patient. Data from individual and aggregated case series were extracted from each article.

Pituitary hemangioblastoma in a patient with von Hippel-Lindau disease. Not infrequently the mural nodule itself has cystic cfrebral within it. Hemangioblastoma of the lateral ventricle: Polycystic kidneys were found in the same two men as were cysts in the pancreas of each. Astrocytes in hemangioblastomas of the central nervous system and their relationship to stromal cells.

Rate of progression-free survival among patients with cystic tumors and solid tumors. An unusual case of a highly progressive supratentorial capillary haemangioblastoma – histopathological considerations. Clinical course of retrobulbar hemangioblastomas in von Hippel-Lindau disease.


Case study and ultrastructural characteristics. Where possible, we performed statistical analysis to determine the efficacy of various treatment approaches using the existing body of published patient data.


From Wikipedia, the free encyclopedia. In September,examination showed a large right retinal hemangioma, dysarthria, and dysmetria of the right arm.

Hemangioblastoma – Wikipedia

Supratentorial cystic hemangioblastoma with infratentorial extension—a unique location and a rare infant case. The outcome for hemangioblastoma is very good, if surgical extraction of the tumor can be achieved; excision is possible in most cases and permanent neurologic deficit is uncommon and can be avoided altogether if the tumor is diagnosed and treated early.

The microscopic differentiation between the tumors is less well-defined. He also hemangioblastlma retinal angiomatosis and a family history of hemangioblastic tumors. Log in Sign up. Our principle goal was to identify features of these tumors that would not be immediately obvious by reading isolated case reports.

Cerebral Hemangioblastoma Occurring in a Patient with von Hippel-Lindau Disease

Unusual, rod-shaped cytoplasmic inclusions Hirano bodies in a cerebellar hemangioblastoma. Case 19 Case Of more importance, among 14 tumors with documented serial imaging, 13 tumors showed growth, suggesting that these tumors show high propensity for growth. In the past, diagnosis has depended upon the topographical location of the tumor in relation to the tentorium cerebelli.

Cerebral hemangioblastoma occurring in a patient with von Hippel-Lindau disease. Suprasellar hemangioblastoma in a patient with von Hippel-Lindau disease confirmed by germline mutation study: Hemangioblastoma is currently considered to be a grade I meningeal neoplasm of uncertain origin according to the latest World Health Organization classification of CNS tumors.


Case 17 Case Aggressive leptomeningeal hemangioblastomatosis of the central nervous system in a patient with von Hippel-Lindau disease. From individual and collective experience, it is recognized that these lesions may be multiple in the cerebellum. There was a trend toward significance in the association between presence of cysts and PFS; patients with cystic tumors were less likely to present with progression than were those with solid tumors 5-year PFS: Kaplan-Meier analysis was used to generate time to progression curves.

On exploration of the posterior fossa, a new left cerebellar neoplasm in the wall of a cyst was found and excised.

Neuroblastoma Esthesioneuroblastoma Ganglioneuroblastoma Medulloblastoma Atypical teratoid rhabdoid tumor. Diagnosis of von Hippel-Lindau disease in a patient with blindness resulting from bilateral optic nerve hemangioblastomas.

These tumours generally present on imaging as sharply demarcated homogeneous masses composed of a cyst with non-enhancing walls, a mural nodule which vividly enhances, often with prominent serpentine flow voids.

Highlights from the Literature.

Although they can occur in any section of the central nervous systemthey usually occur in either side of the cerebellumthe brain stem or the spinal cord. Read it at Henangioblastoma Books – Find it at Amazon.